Successful treatment of pigmented dermatofibrosarcoma protuberance on the nasal root with cyberknife radiosurgery.

© 2012 The Authors. doi: 10.2340/00015555-1357 Journal Compilation © 2012 Acta Dermato-Venereologica. ISSN 0001-5555 Dermatofibrosarcoma protuberans (DFSP) is a fibrohistiocytic tumour of intermediate malignancy characterized by slow infiltrative growth and a high tendency to recur locally. Pigmented DFSP, also known as Bednar tumour, is a rare variant of DFSP and accounts for up to 5% of all DFSPs. DFSP occurs predominantly on the trunk, back and proximal extremities, with 12–15% of the cases localized in the head and neck region (1). When the lesions are located near critical facial structures, standard surgical therapy with a wide margin is impractical for cosmetic and functional reasons. We describe here the successful treatment of a pigmented DFSP on the nasal root with CyberKnife radiosurgery.